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Intravenous Immunoglobulin in Lupus Panniculitis

Identifieur interne : 001859 ( Main/Exploration ); précédent : 001858; suivant : 001860

Intravenous Immunoglobulin in Lupus Panniculitis

Auteurs : João Espírito Santo [Portugal] ; M. F. Gomes [Portugal] ; M. J. Gomes [Portugal] ; L. Peixoto [Portugal] ; S. C. Pereira [Portugal] ; A. Acabado [Portugal] ; J. Freitas [Portugal] ; G. Vinhas De Sousa [Portugal]

Source :

RBID : ISTEX:DCAC39A9829CF6CCCF31537E959F88B5AF6A35F9

English descriptors

Abstract

Abstract: Systemic lupus erythematosus (SLE) is a disease of unknown cause that may involve one or many organ or systems. Skin involvement is a major feature in this disease, and a wide variety of skin conditions may be present. Lupus erythematosus panniculitis (LEP) constitutes a rare form of cutaneous lupus characterized by recurrent nodular or plaque lesions that can vary from a benign and mild course to a more disfiguring disease. Initial therapy includes corticosteroids, antimalarials, and azathioprine and, in refractory cases, two antimalarials in association, mycophenolate mofetil, or other immunomodulators. Intravenous immuglobulin (IVIG) is used in many autoimmune disorders, like in SLE, although clinical trials have not yet taken place. In this report, we review skin manifestations of SLE and their treatment, IVIG, and finally a case of LEP successfully treated with IVIG when other therapy modalities failed.

Url:
DOI: 10.1007/s12016-009-8162-x


Affiliations:


Links toward previous steps (curation, corpus...)


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<div type="abstract" xml:lang="en">Abstract: Systemic lupus erythematosus (SLE) is a disease of unknown cause that may involve one or many organ or systems. Skin involvement is a major feature in this disease, and a wide variety of skin conditions may be present. Lupus erythematosus panniculitis (LEP) constitutes a rare form of cutaneous lupus characterized by recurrent nodular or plaque lesions that can vary from a benign and mild course to a more disfiguring disease. Initial therapy includes corticosteroids, antimalarials, and azathioprine and, in refractory cases, two antimalarials in association, mycophenolate mofetil, or other immunomodulators. Intravenous immuglobulin (IVIG) is used in many autoimmune disorders, like in SLE, although clinical trials have not yet taken place. In this report, we review skin manifestations of SLE and their treatment, IVIG, and finally a case of LEP successfully treated with IVIG when other therapy modalities failed.</div>
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